Research Use Only. KIRhub outputs are computational research artifacts. They are not validated for clinical decision-making, diagnosis, or treatment.

82930

EPN · Supratentorial EPN

5dd17c72-5a55-5188-8cbf-bde79bf5efbc

Score in workbench →

Clinical attributes

From the source cohort, normalized into canonical keys plus the project's native columns.

cancer_type
EPN
cancer_type_detailed
subtype
Supratentorial EPN
cancer_type
EPN
subtype
Supratentorial EPN
age_years
8
fusion
ZFTA_RELA
e1_e2
E1
umap1_2d
-3.453921603
umap2_2d
2.427916002
umap1_3d
-0.689516756
umap2_3d
3.221470169
umap3_3d
-1.724357759
dataset
EPN-Felix

GSVA pathway preview (50 Hallmark scores)

MeasuredDerivedReference

Top 10 most elevated and top 10 most suppressed Hallmark pathways for this sample.

Top 10 elevated

  • PANCREAS_BETA_CELLS+0.370
  • NOTCH_SIGNALING+0.310
  • G2M_CHECKPOINT+0.300
  • E2F_TARGETS+0.290
  • PEROXISOME+0.220
  • ESTROGEN_RESPONSE_LATE+0.210
  • HEDGEHOG_SIGNALING+0.190
  • BILE_ACID_METABOLISM+0.180
  • REACTIVE_OXYGEN_SPECIES_PATHWAY+0.180
  • WNT_BETA_CATENIN_SIGNALING+0.170

Top 10 suppressed

  • TNFA_SIGNALING_VIA_NFKB-0.330
  • PROTEIN_SECRETION-0.310
  • CHOLESTEROL_HOMEOSTASIS-0.290
  • ANGIOGENESIS-0.270
  • MYC_TARGETS_V2-0.260
  • ANDROGEN_RESPONSE-0.250
  • UV_RESPONSE_DN-0.230
  • UNFOLDED_PROTEIN_RESPONSE-0.210
  • DNA_REPAIR-0.200
  • MYC_TARGETS_V1-0.190

Patient twins — nearest pathway neighbors

MeasuredDerived

10 samples closest to this one in 50-dim pathway space, drawn from the Pathway Atlas. Cosine similarity = 1 means identical pathway state.

6 twins match this tumor's tissue · 4 come from a different tissue of origin

#SampleCancer typeSubtypecos similarity
1BS_ZVWE73JZ
brain-umap@2
high-grade glioma0.684
2MNG340
mng-umap@100
0.654
3BS_V3Z3DB4N
brain-umap@2
high-grade glioma0.617
4MNG1086
mng-umap@100
0.610
5SRR33532783
breast-umap@18
C0.592
6BS_3MS8WVNR
brain-umap@2
high-grade glioma0.583
7s0099994
melanoma-umap@29
0.580
8MNG222
mng-umap@100
0.570
9MDT-AP-2806
medullo-epn-umap@date-based
MedMedulloblastoma0.559
10MNG1292
mng-umap@100
0.558

Per-pathway drug coverage

ModeledCalibratedDerived

For each elevated pathway in this tumor, the best-reversing drug across the catalog. Uncovered pathways = unmet need at pathway level for this one patient.

0 of 21 elevated pathways have at least one drug that meaningfully reverses them.

Pathway (elevated)tumor scoreBest drugreversal magnitude
PANCREAS_BETA_CELLS0.370Cobimetinib— uncovered
NOTCH_SIGNALING0.310Inavolisib— uncovered
G2M_CHECKPOINT0.300Inavolisib— uncovered
E2F_TARGETS0.290Inavolisib— uncovered
PEROXISOME0.220Idelalisib— uncovered
ESTROGEN_RESPONSE_LATE0.210Idelalisib— uncovered
HEDGEHOG_SIGNALING0.190Inavolisib— uncovered
BILE_ACID_METABOLISM0.180Inavolisib— uncovered
REACTIVE_OXYGEN_SPECIES_PATHWAY0.180Inavolisib— uncovered
WNT_BETA_CATENIN_SIGNALING0.170Inavolisib— uncovered
ESTROGEN_RESPONSE_EARLY0.150Inavolisib— uncovered
INTERFERON_ALPHA_RESPONSE0.120Inavolisib— uncovered
KRAS_SIGNALING_DN0.110Remibrutinib— uncovered
SPERMATOGENESIS0.110Inavolisib— uncovered
COAGULATION0.050Binimetinib— uncovered
P53_PATHWAY0.050Idelalisib— uncovered
HEME_METABOLISM0.040Temsirolimus— uncovered
COMPLEMENT0.020Inavolisib— uncovered
APICAL_JUNCTION0.010Inavolisib— uncovered
INTERFERON_GAMMA_RESPONSE0.010Idelalisib— uncovered