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ABL1 (Y253H)

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ABL1 · Variant type: point · HGVS: p.Y253H

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Bosutinib100.0%0.0%87.22
2Ponatinib100.0%0.0%78.23
3Nintedanib99.5%0.5%90.23
4Dasatinib99.1%0.9%87.97
5Vandetanib97.4%2.6%95.74
6Canertinib95.5%4.5%96.49
7Axitinib95.1%4.9%93.23
8Nilotinib95.0%5.0%96.49
9Repotrectinib93.9%6.1%84.21
10Crizotinib91.5%8.5%91.39
11Pacritinib90.8%9.2%88.64
12Brigatinib90.6%9.4%82.96
13Erdafitinib87.8%12.2%95.71
14Dacomitinib82.5%17.5%97.99
15Tivozanib81.0%19.0%92.42
16Erlotinib78.0%22.0%99.75
17Lenvatinib73.5%26.5%97.74
18Sunitinib71.2%28.8%91.73
19Fedratinib70.0%30.0%96.21
20Afatinib68.4%31.6%98.50
21Alectinib64.9%35.1%95.49
22Ripretinib62.9%37.1%92.95
23Entrectinib62.4%37.6%93.69
24Gilteritinib55.2%44.8%88.97
25Avapritinib54.2%45.8%97.73

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Bosutinib100.0%99.7%+0.3%
Ponatinib100.0%100.0%+0.0%
Nintedanib99.5%99.9%-0.4%
Dasatinib99.1%98.6%+0.5%
Vandetanib97.4%95.7%+1.7%
Canertinib95.5%91.6%+3.9%
Axitinib95.1%99.4%-4.4%
Nilotinib95.0%98.0%-3.0%
Repotrectinib93.9%93.6%+0.3%
Crizotinib91.5%97.0%-5.5%
Pacritinib90.8%92.0%-1.2%
Brigatinib90.6%82.8%+7.8%
Erdafitinib87.8%90.9%-3.1%
Dacomitinib82.5%80.8%+1.7%
Tivozanib81.0%95.8%-14.8%
Erlotinib78.0%
Lenvatinib73.5%76.3%-2.9%
Sunitinib71.2%
Fedratinib70.0%82.7%-12.7%
Afatinib68.4%
Alectinib64.9%
Ripretinib62.9%82.9%-20.0%
Entrectinib62.4%
Gilteritinib55.2%
Avapritinib54.2%

Cancer associations

CancerOrganSource
haematopoietic_neoplasm_haematopoietic_and_lymphoid_tissueBlood/Lymphatic Systemref
lymphoid_neoplasm_haematopoietic_and_lymphoid_tissueBlood/Lymphatic Systemref
carcinoma_breastBreastref

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