Research Use Only. KIRhub outputs are computational research artifacts. They are not validated for clinical decision-making, diagnosis, or treatment.

82956

EPN · Supratentorial EPN

14bf8ccc-8e6b-55cf-841a-a98984303bf2

Score in workbench →

Clinical attributes

From the source cohort, normalized into canonical keys plus the project's native columns.

cancer_type
EPN
cancer_type_detailed
subtype
Supratentorial EPN
cancer_type
EPN
subtype
Supratentorial EPN
age_years
2
fusion
ZFTA_RELA
e1_e2
E1
umap1_2d
-3.046833854
umap2_2d
1.221564776
umap1_3d
0.329512546
umap2_3d
2.971384258
umap3_3d
-2.434326173
dataset
EPN-Felix

GSVA pathway preview (50 Hallmark scores)

MeasuredDerivedReference

Top 10 most elevated and top 10 most suppressed Hallmark pathways for this sample.

Top 10 elevated

  • OXIDATIVE_PHOSPHORYLATION+0.530
  • PROTEIN_SECRETION+0.410
  • MYC_TARGETS_V1+0.380
  • UNFOLDED_PROTEIN_RESPONSE+0.380
  • DNA_REPAIR+0.370
  • CHOLESTEROL_HOMEOSTASIS+0.310
  • INTERFERON_ALPHA_RESPONSE+0.300
  • MTORC1_SIGNALING+0.290
  • FATTY_ACID_METABOLISM+0.280
  • MYC_TARGETS_V2+0.270

Top 10 suppressed

  • EPITHELIAL_MESENCHYMAL_TRANSITION-0.370
  • KRAS_SIGNALING_UP-0.320
  • HYPOXIA-0.290
  • KRAS_SIGNALING_DN-0.290
  • ALLOGRAFT_REJECTION-0.230
  • INFLAMMATORY_RESPONSE-0.220
  • APICAL_JUNCTION-0.210
  • IL6_JAK_STAT3_SIGNALING-0.200
  • COMPLEMENT-0.190
  • PANCREAS_BETA_CELLS-0.170

Patient twins — nearest pathway neighbors

MeasuredDerived

10 samples closest to this one in 50-dim pathway space, drawn from the Pathway Atlas. Cosine similarity = 1 means identical pathway state.

9 twins match this tumor's tissue · 1 come from a different tissue of origin

#SampleCancer typeSubtypecos similarity
1F2FCC449-3487-474C-82A6-8F2ED71E41BC
brain-umap@2
0.828
2MNG434
mng-umap@100
0.817
3EA6A086B-F655-47E8-9E70-8A2D36FC2AE1
brain-umap@2
0.807
4A0DA6087-9D43-41F9-8569-9F9320E4A9E8
brain-umap@2
0.802
5SJBT031392_D1.RNA-Seq
medullo-epn-umap@date-based
EPNEPN Tumor0.795
6MNG570
mng-umap@100
0.784
7BS_CZ3NA7KV
brain-umap@2
Supratentorial Ependymoma0.782
8A6FB1BEE-0D36-480C-8619-1FA82583FCD1
brain-umap@2
0.777
9b2b4cc41-5760-4463-bcde-16115ceb12c2
melanoma-umap@29
0.773
10SRR6013598
lung-landscapes@6
cohortA40.773

Per-pathway drug coverage

ModeledCalibratedDerived

For each elevated pathway in this tumor, the best-reversing drug across the catalog. Uncovered pathways = unmet need at pathway level for this one patient.

0 of 27 elevated pathways have at least one drug that meaningfully reverses them.

Pathway (elevated)tumor scoreBest drugreversal magnitude
OXIDATIVE_PHOSPHORYLATION0.530Remibrutinib— uncovered
PROTEIN_SECRETION0.410Remibrutinib— uncovered
MYC_TARGETS_V10.380Inavolisib— uncovered
UNFOLDED_PROTEIN_RESPONSE0.380Idelalisib— uncovered
DNA_REPAIR0.370Idelalisib— uncovered
CHOLESTEROL_HOMEOSTASIS0.310Remibrutinib— uncovered
INTERFERON_ALPHA_RESPONSE0.300Inavolisib— uncovered
MTORC1_SIGNALING0.290Inavolisib— uncovered
FATTY_ACID_METABOLISM0.280Inavolisib— uncovered
MYC_TARGETS_V20.270Idelalisib— uncovered
HEME_METABOLISM0.260Temsirolimus— uncovered
REACTIVE_OXYGEN_SPECIES_PATHWAY0.260Inavolisib— uncovered
ADIPOGENESIS0.250Inavolisib— uncovered
PI3K_AKT_MTOR_SIGNALING0.240Inavolisib— uncovered
UV_RESPONSE_UP0.160Idelalisib— uncovered
ANDROGEN_RESPONSE0.130Inavolisib— uncovered
UV_RESPONSE_DN0.130Inavolisib— uncovered
WNT_BETA_CATENIN_SIGNALING0.120Inavolisib— uncovered
P53_PATHWAY0.110Idelalisib— uncovered
SPERMATOGENESIS0.100Inavolisib— uncovered