Research Use Only. KIRhub outputs are computational research artifacts. They are not validated for clinical decision-making, diagnosis, or treatment.

BS_KE56MMY0

Neurofibroma

7b85d37d-ff2a-556a-8e68-edc9ff5dfcd1

Score in workbench →

Clinical attributes

From the source cohort, normalized into canonical keys plus the project's native columns.

cancer_type
Neurofibroma
cancer_type_detailed
subtype
cancer_type
Neurofibroma
overall_survival_months
19.316688567674113
age_years
17.392
sex
Male

GSVA pathway preview (50 Hallmark scores)

MeasuredDerivedReference

Top 10 most elevated and top 10 most suppressed Hallmark pathways for this sample.

Top 10 elevated

  • MYC_TARGETS_V1+0.503
  • EPITHELIAL_MESENCHYMAL_TRANSITION+0.486
  • G2M_CHECKPOINT+0.469
  • MYC_TARGETS_V2+0.459
  • E2F_TARGETS+0.456
  • IL6_JAK_STAT3_SIGNALING+0.413
  • TNFA_SIGNALING_VIA_NFKB+0.402
  • ALLOGRAFT_REJECTION+0.390
  • INTERFERON_GAMMA_RESPONSE+0.385
  • REACTIVE_OXYGEN_SPECIES_PATHWAY+0.365

Top 10 suppressed

  • HEDGEHOG_SIGNALING-0.376
  • KRAS_SIGNALING_DN-0.294
  • BILE_ACID_METABOLISM-0.220
  • MYOGENESIS-0.197
  • PANCREAS_BETA_CELLS-0.184
  • SPERMATOGENESIS-0.109
  • ESTROGEN_RESPONSE_LATE-0.071
  • XENOBIOTIC_METABOLISM-0.069
  • HEME_METABOLISM-0.050
  • UV_RESPONSE_UP-0.045

Patient twins — nearest pathway neighbors

MeasuredDerived

10 samples closest to this one in 50-dim pathway space, drawn from the Pathway Atlas. Cosine similarity = 1 means identical pathway state.

10 twins match this tumor's tissue · 0 come from a different tissue of origin

#SampleCancer typeSubtypecos similarity
1F873381B-3D15-47B2-9385-080590B316B7
brain-umap@2
0.957
2SRR934932
brain-umap@2
0.952
38B4E465B-0FD5-4154-824B-1E6B2656FD2F
brain-umap@2
0.951
4SRR934839
brain-umap@2
0.948
5SRR934837
brain-umap@2
0.946
6SRR934958
brain-umap@2
0.940
7SRR934730
brain-umap@2
0.939
8SRR934925
brain-umap@2
0.931
9SRR934965
brain-umap@2
0.931
1065F93AB7-AA99-49B5-8D59-7D0DE9CA9E34
brain-umap@2
0.931

Per-pathway drug coverage

ModeledCalibratedDerived

For each elevated pathway in this tumor, the best-reversing drug across the catalog. Uncovered pathways = unmet need at pathway level for this one patient.

0 of 38 elevated pathways have at least one drug that meaningfully reverses them.

Pathway (elevated)tumor scoreBest drugreversal magnitude
MYC_TARGETS_V10.503Inavolisib— uncovered
EPITHELIAL_MESENCHYMAL_TRANSITION0.486Inavolisib— uncovered
G2M_CHECKPOINT0.469Inavolisib— uncovered
MYC_TARGETS_V20.459Idelalisib— uncovered
E2F_TARGETS0.456Inavolisib— uncovered
IL6_JAK_STAT3_SIGNALING0.413Inavolisib— uncovered
TNFA_SIGNALING_VIA_NFKB0.402Inavolisib— uncovered
ALLOGRAFT_REJECTION0.390Idelalisib— uncovered
INTERFERON_GAMMA_RESPONSE0.385Idelalisib— uncovered
REACTIVE_OXYGEN_SPECIES_PATHWAY0.365Inavolisib— uncovered
APOPTOSIS0.352Idelalisib— uncovered
INFLAMMATORY_RESPONSE0.352Idelalisib— uncovered
UNFOLDED_PROTEIN_RESPONSE0.351Idelalisib— uncovered
DNA_REPAIR0.346Idelalisib— uncovered
INTERFERON_ALPHA_RESPONSE0.334Inavolisib— uncovered
ANGIOGENESIS0.329Remibrutinib— uncovered
MTORC1_SIGNALING0.328Inavolisib— uncovered
TGF_BETA_SIGNALING0.324Inavolisib— uncovered
PI3K_AKT_MTOR_SIGNALING0.311Inavolisib— uncovered
PROTEIN_SECRETION0.307Remibrutinib— uncovered