Research Use Only. KIRhub outputs are computational research artifacts. They are not validated for clinical decision-making, diagnosis, or treatment.

BS_D4PJYHZ2

Neurofibroma

80780d75-27a9-5e82-9d97-2d121fd50bc2

Score in workbench →

Clinical attributes

From the source cohort, normalized into canonical keys plus the project's native columns.

cancer_type
Neurofibroma
cancer_type_detailed
subtype
cancer_type
Neurofibroma
overall_survival_months
8.015768725361367
age_years
12.786
sex
Female

GSVA pathway preview (50 Hallmark scores)

MeasuredDerivedReference

Top 10 most elevated and top 10 most suppressed Hallmark pathways for this sample.

Top 10 elevated

  • INTERFERON_ALPHA_RESPONSE+0.446
  • ANGIOGENESIS+0.441
  • APICAL_JUNCTION+0.402
  • COAGULATION+0.399
  • EPITHELIAL_MESENCHYMAL_TRANSITION+0.386
  • IL6_JAK_STAT3_SIGNALING+0.379
  • INTERFERON_GAMMA_RESPONSE+0.375
  • WNT_BETA_CATENIN_SIGNALING+0.370
  • APICAL_SURFACE+0.366
  • MYOGENESIS+0.335

Top 10 suppressed

  • E2F_TARGETS-0.534
  • MTORC1_SIGNALING-0.492
  • G2M_CHECKPOINT-0.474
  • OXIDATIVE_PHOSPHORYLATION-0.467
  • PROTEIN_SECRETION-0.451
  • MYC_TARGETS_V1-0.444
  • SPERMATOGENESIS-0.354
  • UNFOLDED_PROTEIN_RESPONSE-0.280
  • PANCREAS_BETA_CELLS-0.223
  • MYC_TARGETS_V2-0.215

Patient twins — nearest pathway neighbors

MeasuredDerived

10 samples closest to this one in 50-dim pathway space, drawn from the Pathway Atlas. Cosine similarity = 1 means identical pathway state.

9 twins match this tumor's tissue · 1 come from a different tissue of origin

#SampleCancer typeSubtypecos similarity
1BS_5P3CZQV8
brain-umap@2
Neurofibroma0.953
2BS_Z28VKGNS
brain-umap@2
Neurofibroma0.943
3BS_FQX1PRAJ
brain-umap@2
Neurofibroma0.940
4BS_TQ5QHR17
brain-umap@2
Neurofibroma0.938
5BS_69V8P8A0
brain-umap@2
Neurofibroma0.927
6BS_TAHV8N04
brain-umap@2
Neurofibroma0.925
7BS_FRM9TG02
brain-umap@2
Neurofibroma0.924
8BS_GDHH6T5A
brain-umap@2
Neurofibroma0.923
9TCGA-A2-A0CO-01A-13R-A22K-07
breast-umap@18
A0.916
10MDT-AP-1125
medullo-epn-umap@date-based
MedMedulloblastoma0.910

Per-pathway drug coverage

ModeledCalibratedDerived

For each elevated pathway in this tumor, the best-reversing drug across the catalog. Uncovered pathways = unmet need at pathway level for this one patient.

0 of 28 elevated pathways have at least one drug that meaningfully reverses them.

Pathway (elevated)tumor scoreBest drugreversal magnitude
INTERFERON_ALPHA_RESPONSE0.446Inavolisib— uncovered
ANGIOGENESIS0.441Remibrutinib— uncovered
APICAL_JUNCTION0.402Inavolisib— uncovered
COAGULATION0.399Binimetinib— uncovered
EPITHELIAL_MESENCHYMAL_TRANSITION0.386Inavolisib— uncovered
IL6_JAK_STAT3_SIGNALING0.379Inavolisib— uncovered
INTERFERON_GAMMA_RESPONSE0.375Idelalisib— uncovered
WNT_BETA_CATENIN_SIGNALING0.370Inavolisib— uncovered
APICAL_SURFACE0.366Temsirolimus— uncovered
MYOGENESIS0.335Inavolisib— uncovered
TNFA_SIGNALING_VIA_NFKB0.332Inavolisib— uncovered
IL2_STAT5_SIGNALING0.292Idelalisib— uncovered
ALLOGRAFT_REJECTION0.290Idelalisib— uncovered
INFLAMMATORY_RESPONSE0.284Idelalisib— uncovered
ESTROGEN_RESPONSE_EARLY0.279Inavolisib— uncovered
COMPLEMENT0.251Inavolisib— uncovered
TGF_BETA_SIGNALING0.239Inavolisib— uncovered
ESTROGEN_RESPONSE_LATE0.227Idelalisib— uncovered
KRAS_SIGNALING_UP0.208Inavolisib— uncovered
P53_PATHWAY0.205Idelalisib— uncovered