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FGFR4 (V550L)

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FGFR4 · Variant type: point · HGVS: p.V550L

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Brigatinib92.7%7.3%82.96
2Futibatinib90.3%9.7%98.48
3Ceritinib68.5%31.5%95.44
4Erdafitinib58.6%41.4%95.71
5Pralsetinib54.2%45.8%93.43
6Selpercatinib42.3%57.7%96.72
7Defactinib37.4%62.6%92.68
8Upadacitinib32.8%67.2%97.98
9Alectinib30.4%69.6%95.49
10Fedratinib29.9%70.1%96.21
11Pemigatinib28.1%71.9%98.23
12Alpelisib26.2%73.8%97.22
13Sunitinib25.9%74.1%91.73
14Repotrectinib20.7%79.3%84.21
15Ponatinib19.6%80.4%78.23
16Pacritinib18.8%81.2%88.64
17Entrectinib18.4%81.6%93.69
18Neratinib12.2%87.8%93.18
19Infigratinib10.1%89.9%98.24
20Pirtobrutinib8.2%91.8%99.49
21Trametinib8.1%91.9%99.50
22Tenalisib7.8%92.2%97.98
23Nintedanib7.4%92.6%90.23
24Apatinib7.1%92.9%97.73
25Gilteritinib6.9%93.1%88.97

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Brigatinib92.7%73.3%+19.4%
Futibatinib90.3%97.9%-7.7%
Ceritinib68.5%48.2%+20.3%
Erdafitinib58.6%98.0%-39.5%
Pralsetinib54.2%64.6%-10.4%
Selpercatinib42.3%49.1%-6.9%
Defactinib37.4%
Upadacitinib32.8%
Alectinib30.4%36.3%-5.9%
Fedratinib29.9%
Pemigatinib28.1%93.9%-65.8%
Alpelisib26.2%96.8%-70.6%
Sunitinib25.9%
Repotrectinib20.7%
Ponatinib19.6%96.7%-77.1%
Pacritinib18.8%
Entrectinib18.4%
Neratinib12.2%
Infigratinib10.1%94.7%-84.7%
Pirtobrutinib8.2%
Trametinib8.1%
Tenalisib7.8%83.9%-76.1%
Nintedanib7.4%33.7%-26.4%
Apatinib7.1%
Gilteritinib6.9%

Cancer associations

CancerOrganSource
rhabdomyosarcoma_soft_tissueSoft Tissueref
carcinoma_breastBreastref
malignant_fibrous_histiocytoma-pleomorphic_sarcoma_soft_tissueSoft Tissueref
carcinoma_endometriumUterusref
UCEC-USUterusref
UCECUterusref

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