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PDGFRa (V561D)

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PDGFRA · Variant type: point · HGVS: p.V561D

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Ponatinib99.7%0.3%78.23
2Nilotinib98.6%1.4%96.49
3Avapritinib98.3%1.7%97.73
4Sorafenib98.2%1.8%96.72
5Dasatinib98.2%1.8%87.97
6Tivozanib97.4%2.6%92.42
7Nintedanib96.9%3.1%90.23
8Imatinib96.9%3.1%99.00
9Axitinib94.8%5.2%93.23
10Regorafenib94.3%5.7%95.99
11Erdafitinib90.8%9.2%95.71
12Lenvatinib87.5%12.5%97.74
13Sunitinib84.7%15.3%91.73
14Cabozantinib84.3%15.8%92.73
15Ripretinib82.3%17.7%92.95
16Selpercatinib82.1%17.9%96.72
17Pazopanib79.5%20.5%97.49
18Quizartinib78.7%21.3%99.50
19Pexidartinib71.6%28.4%99.49
20Vandetanib71.3%28.7%95.74
21Apatinib70.5%29.5%97.73
22Vemurafenib70.0%30.0%96.49
23Fedratinib69.2%30.8%96.21
24Umbralisib66.2%33.8%98.74
25Brigatinib66.0%34.0%82.96

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Ponatinib99.7%100.0%-0.3%
Nilotinib98.6%97.9%+0.7%
Avapritinib98.3%99.1%-0.9%
Sorafenib98.2%95.6%+2.6%
Dasatinib98.2%98.3%-0.1%
Tivozanib97.4%96.9%+0.5%
Nintedanib96.9%98.3%-1.4%
Imatinib96.9%98.9%-2.0%
Axitinib94.8%96.0%-1.2%
Regorafenib94.3%96.7%-2.3%
Erdafitinib90.8%94.5%-3.7%
Lenvatinib87.5%88.0%-0.5%
Sunitinib84.7%84.2%+0.5%
Cabozantinib84.3%79.3%+5.0%
Ripretinib82.3%81.5%+0.8%
Selpercatinib82.1%
Pazopanib79.5%74.5%+5.0%
Quizartinib78.7%
Pexidartinib71.6%
Vandetanib71.3%82.0%-10.7%
Apatinib70.5%
Vemurafenib70.0%
Fedratinib69.2%
Umbralisib66.2%
Brigatinib66.0%

Cancer associations

CancerOrganSource
gastrointestinal_stromal_tumour_soft_tissueSoft Tissueref
other_stomachStomach/Digestive Tractref
other_small_intestineSmall Intestineref

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