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PDGFRa (D842V)

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PDGFRA · Variant type: point · HGVS: p.D842V

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Avapritinib99.6%0.4%97.73
2Ponatinib98.6%1.4%78.23
3Nintedanib98.3%1.7%90.23
4Dasatinib94.9%5.1%87.97
5Brigatinib94.0%6.0%82.96
6Erdafitinib92.5%7.5%95.71
7Vandetanib91.5%8.4%95.74
8Pralsetinib87.4%12.6%93.43
9Mitapivat87.0%13.0%100.00
10Sunitinib84.4%15.6%91.73
11Ripretinib83.9%16.1%92.95
12Selpercatinib82.6%17.4%96.72
13Canertinib80.5%19.4%96.49
14Gilteritinib79.5%20.5%88.97
15Pacritinib72.5%27.5%88.64
16Tivozanib66.9%33.1%92.42
17Axitinib65.1%34.9%93.23
18Bosutinib64.3%35.7%87.22
19Fostamatinib64.3%35.8%96.74
20Dacomitinib63.6%36.4%97.99
21Alectinib53.3%46.7%95.49
22Pazopanib51.9%48.1%97.49
23Sorafenib49.6%50.4%96.72
24Imatinib46.6%53.4%99.00
25Osimertinib41.7%58.3%97.24

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Avapritinib99.6%99.1%+0.5%
Ponatinib98.6%100.0%-1.4%
Nintedanib98.3%98.3%+0.0%
Dasatinib94.9%98.3%-3.4%
Brigatinib94.0%
Erdafitinib92.5%94.5%-2.1%
Vandetanib91.5%82.0%+9.6%
Pralsetinib87.4%
Mitapivat87.0%
Sunitinib84.4%84.2%+0.2%
Ripretinib83.9%81.5%+2.3%
Selpercatinib82.6%
Canertinib80.5%
Gilteritinib79.5%78.1%+1.4%
Pacritinib72.5%
Tivozanib66.9%96.9%-30.1%
Axitinib65.1%96.0%-30.9%
Bosutinib64.3%
Fostamatinib64.3%
Dacomitinib63.6%
Alectinib53.3%
Pazopanib51.9%74.5%-22.7%
Sorafenib49.6%95.6%-46.0%
Imatinib46.6%98.9%-52.3%
Osimertinib41.7%

Cancer associations

CancerOrganSource
gastrointestinal_stromal_tumour_soft_tissueSoft Tissueref
carcinoma_large_intestineLarge Intestineref
other_stomachStomach/Digestive Tractref
other_small_intestineSmall Intestineref
glioma_central_nervous_systemBrain/CNSref
gastrointestinal_stromal_tumour_large_intestineLarge Intestineref
other_large_intestineLarge Intestineref
lymphoid_neoplasm_haematopoietic_and_lymphoid_tissueBlood/Lymphatic Systemref
other_gastrointestinal_tract_(site_indeterminate)Soft Tissueref
haematopoietic_neoplasm_haematopoietic_and_lymphoid_tissueBlood/Lymphatic Systemref
carcinoma_breastBreastref

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