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ALK2 (Q207D)

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ACVR1 · Variant type: point · HGVS: p.Q207D

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Pacritinib97.5%2.5%88.64
2Fedratinib77.7%22.3%96.21
3Dabrafenib70.7%29.3%94.74
4Crizotinib57.3%42.7%91.39
5Gilteritinib55.5%44.5%88.97
6Nintedanib54.4%45.6%90.23
7Dasatinib53.8%46.2%87.97
8Pralsetinib21.9%78.1%93.43
9Selpercatinib11.0%89.0%96.72
10Fostamatinib9.8%90.2%96.74
11Osimertinib9.5%90.5%97.24
12Imatinib9.2%90.8%99.00
13Selumetinib7.8%92.2%100.00
14Gefitinib7.8%92.2%99.25
15Infigratinib7.7%92.3%98.24
16Leniolisib7.3%92.7%100.00
17Trametinib7.2%92.8%99.50
18Apatinib6.4%93.6%97.73
19Lazertinib6.3%93.7%97.47
20Capmatinib6.1%93.9%99.75
21Ceritinib6.0%94.0%95.44
22Baricitinib4.9%95.1%97.99
23Umbralisib4.9%95.1%98.74
24Sirolimus4.5%95.5%100.00
25Bosutinib4.5%95.5%87.22

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Pacritinib97.5%
Fedratinib77.7%
Dabrafenib70.7%
Crizotinib57.3%
Gilteritinib55.5%
Nintedanib54.4%
Dasatinib53.8%
Pralsetinib21.9%
Selpercatinib11.0%
Fostamatinib9.8%
Osimertinib9.5%
Imatinib9.2%
Selumetinib7.8%
Gefitinib7.8%
Infigratinib7.7%
Leniolisib7.3%
Trametinib7.2%
Apatinib6.4%
Lazertinib6.3%
Capmatinib6.1%
Ceritinib6.0%
Baricitinib4.9%
Umbralisib4.9%
Sirolimus4.5%
Bosutinib4.5%

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