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PDGFRa (G680R)

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PDGFRA · Variant type: point · HGVS: p.G680R

Drug response on this variant

#DrugInhibition on variantResidualKISS
1Sorafenib96.5%3.5%96.72
2Tivozanib95.0%5.0%92.42
3Ripretinib87.1%12.9%92.95
4Avapritinib75.4%24.6%97.73
5Apatinib68.5%31.5%97.73
6Sunitinib63.1%36.9%91.73
7Selpercatinib48.3%51.7%96.72
8Erdafitinib43.5%56.5%95.71
9Quizartinib34.6%65.4%99.50
10Pexidartinib29.8%70.2%99.49
11Pralsetinib26.0%74.0%93.43
12Defactinib21.2%78.8%92.68
13Umbralisib20.4%79.6%98.74
14Fedratinib18.1%81.9%96.21
15Infigratinib17.8%82.2%98.24
16Paxalisib16.2%83.8%99.75
17Tenalisib13.1%86.9%97.98
18Gedatolisib12.4%87.6%99.75
19Upadacitinib11.9%88.1%97.98
20Rabusertib10.8%89.2%98.74
21Repotrectinib10.3%89.7%84.21
22Neratinib10.2%89.8%93.18
23Pirtobrutinib9.9%90.1%99.49
24Leniolisib9.0%91.0%100.00
25Lazertinib8.6%91.4%97.47

Wild-type vs variant — drug response delta

Positive Δ means the drug hits the variant harder than wild-type (mutation-selective); negative Δ means it loses potency (resistance).

DrugVariant inhWT inhΔ (variant − WT)
Sorafenib96.5%95.6%+0.9%
Tivozanib95.0%96.9%-1.9%
Ripretinib87.1%81.5%+5.6%
Avapritinib75.4%99.1%-23.7%
Apatinib68.5%
Sunitinib63.1%84.2%-21.0%
Selpercatinib48.3%
Erdafitinib43.5%94.5%-51.1%
Quizartinib34.6%
Pexidartinib29.8%
Pralsetinib26.0%
Defactinib21.2%
Umbralisib20.4%
Fedratinib18.1%
Infigratinib17.8%
Paxalisib16.2%
Tenalisib13.1%
Gedatolisib12.4%
Upadacitinib11.9%
Rabusertib10.8%
Repotrectinib10.3%
Neratinib10.2%
Pirtobrutinib9.9%
Leniolisib9.0%
Lazertinib8.6%

Cancer associations

CancerOrganSource
gastrointestinal_stromal_tumour_soft_tissueSoft Tissueref
AML-USBlood/Lymphatic Systemref

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